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Query: UMLS:C0729233 (
Thoracic
)
6,478
document(s) hit in 31,850,051 MEDLINE articles (0.00 seconds)
A metastatic
synovial sarcoma
in the right atrium and ventricle is described. A 36-year-old man was admitted to our hospital with generalized fatigue, dyspnoea, and precordial pain. Transthoracic echocardiography demonstrated a metastatic tumour in both the right atrium and right ventricle and revealed obstruction of the inflow tract of the right ventricle caused by a metastatic right atrial tumour.
Thoracic
computed tomography revealed a pleural-based paravertebral mass in the left intrathoracic cavity and multiple pulmonary nodules in both lungs. Cardiac surgery was performed for palliative treatment due to right cardiac failure and a risk of fatal embolization. The patient died 12 months after the cardiac surgery.
...
PMID:Synovial sarcoma in the right atrium and right ventricle. 2159 92
Introduction:
Synovial sarcoma
is a rare mesenchymal malignant neoplasm that accounts for less than 10% of soft tissue sarcomas. About 95% of the sarcomas occur in the extremities. Primary synovial sarcomas of the spine are a rare tumor arising from the paravertebral regions, paraspinal muscles or epidural spaces.
Purpose:
To report an atypical radiological presentation of
synovial sarcoma
of the thoracic spine mimicking a nerve sheath tumor in an elderly adult and describe the management with review of the literature.
Clinical presentation:
A forty-six-year-old lady presented with clinical features of a thoracic intradural extramedullary cord compression at T7 level. She was Nurick grade 4 at presentation. MRI of the
Thoracic
spine with whole spine screening showed a contrast enhancing intradural extramedullary tumor at the T7-8 level; the tumor was exiting out through the left T7-8 neural foramina with foraminal widening. The possibility of a schwannoma was considered.
Intervention:
She underwent a T7-8 laminectomy and total excision of the tumor followed by posterior fusion. The biopsy was reported as
synovial sarcoma
. She subsequently underwent radiation and chemotherapy. She had marked improvement in her Neurological status and remained disease free at six months follow-up.
Conclusion:
Synovial sarcoma
of the spine is a rare mesenchymal malignant neoplasm. One needs to consider
Synovial sarcoma
as one of the differential diagnosis of intradural tumors of the spine.
...
PMID:Synovial sarcoma mimicking a thoracic dumbell schwannoma- a case report. 2944 79
