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Query: UMLS:C0403608 (ureter)
 9,655 document(s) hit in 31,850,051 MEDLINE articles (0.00 seconds)

Immediately after birth, a full-term infant was noted to be in severe respiratory distress and died approximately five hours later, despite resuscitative efforts. Postmortem examination revealed agenesis of the trachea with a 1-mm fistula joining the esophagus and the main stem bronchi at the carina. The right kidney, ureter, Fallopian tube, and cornu of the uterus were also absent. The 25 previously reported cases of agenesis of the trachea are summarized, with special emphasis on associated abnormalities.
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PMID:Agenesis of the trachea: report of a case and review of the literature. 94 54

A case is described of a baby girl born with such a large multicystic kidney that it partially obstructed the contralateral ureter, made feeding impossible due to gastric compression, and caused respiratory distress by thoracic cavity compression. Management of the case is described, and a literature review is presented.
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PMID:Neonatal multicystic kidney with associated respiratory distress, obstruction of contralateral ureter, and gastric compromise. 250 27

We describe two boys with the cerebro-costo-mandibular syndrome (CCMS). Both patients presented with Pierre Robin anomaly and respiratory insufficiency and died 12 hours and 10 months after birth. The first boy had muscular hypotonia, severe micrognathia, glossoptosis, short palate, preauricular tag, paraumbilical fibroma, and a small and narrow thorax. His chest roentgenographs showed marked hypoplasia of the first to tenth rib, multiple posterior rib-gaps in the only four ossified ribs. Tracheomalacia and stenosis of the left ureter was observed during autopsy. No structural cerebral anomalies were observed. Respiratory distress necessitated a tracheostomy in the second boy. He had severe micrognathia with glossoptosis and a cleft soft palate were noted. His chest roentgenograph showed a bell-shaped, small thorax with multiple dorsal rib-gap defects. CCMS is a rare disorder often associated with Pierre Robin anomaly. Chest roentgenographs show the typical posterior rib-gap defects, which are quite variable. CCMS usually occurs as an isolated event in a family. Of 41 reported families four reports describe horizontal and two describe vertical transmission of CCMS. This might imply genetic heterogeneity with autosomal recessive and autosomal dominant inheritance. Inter- and intrafamilial expression is variable. Careful family studies are necessary before genetic counseling is given.
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PMID:Cerebro-costo-mandibular syndrome. 888 89

The authors report a case of incidental discovery of a right intrathoracic kidney in a 70-year-old man, in July 1994, on intravenous urography performed for assessment of benign prostatic hyperplasia. This intrathoracic ectopic kidney is due to a diaphragmatic hernia and may be either congenital or acquired. It must be distinguished from true ectopic kidney, present during foetal life [4], which requires a high origin of the renal artery from the aorta with elongation of the ureter. Intrathoracic kidney due to diaphragmatic hernia is usually asymptomatic, but may be responsible for severe clinical symptoms with respiratory distress occurring in a newborn infant with this malformation. The diagnosis of intrathoracic kidney must be considered in the presence of a mediastinal mass on chest x-ray and is confirmed by intravenous urography, or even thoracic computed tomography. Apart from its rare complications, this anomaly does not require any specific treatment.
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PMID:[Intrathoracic kidney due to diaphragmatic hernia: a case report]. 1218 60

Ureteric intussusception is exceptional. The authors report a case of hydronephrosis due to retrograde intussusception of the subpelvic ureter in a 3-month-old boy admitted for respiratory distress syndrome associated with fever of 39 degrees C. Imaging revealed the presence of marked dilatation of the left kidney. Surgical exploration demonstrated hydronephrosis secondary to obstruction due to ureteric intussusception. This is the first case of ureteric intussusception reported in a child.
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PMID:[Hydronephrosis due to retrograde ureteric intussusception]. 1609 62

We report a case of acute respiratory distress syndrome caused by uropathogenic Escherichia coli induced sepsis and treated successfully. A 56-year-old women admitted for high-fever, dyspnea, and disturbance of consciousness on September 11, 2006, was found in chest computed tomography (CT) on admission to have diffuse infiltration with bilateral pleural effusion. Abdominal CT on admission showed left hydronephrosis complicated with ureteral stones. Because of severe hypoxemia, mechanical ventilation was started from hospital day 1. She went into shock soon after admission. Under mechanical ventilation, she was administered several antibiotics and dopamine. Because sera endotoxins were elevated, she was treated by endotoxin adsorption therapy on hospital day 3. A urethral stent was indwelled in the ureter for drainage after endotoxin adsorption therapy. Because Escherichia coli was isolated from urine and blood cultures, she was diagnosed with acute respiratory distress syndrome (ARDS) caused by E. coli inducing septic shock. After therapy, her condition improved, and she was extubated on hospital day 9. Extracorporeal shock wave lithotripsy was conducted on hospital day 19 and she was discharged.
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PMID:[Case of successfully treated acute respiratory distress syndrome complicated by ureteral stones]. 1897 90

We report an uncommon but emerging fungal pathogen, Candida kefyr, as a causative agent of infective endocarditis in a patient with a known history of hypertrophic obstructive cardiomyopathy. A 74-year-old woman with diabetes type II, hypertrophic obstructive cardiomyopathy, presented with gross hematuria and abdominal pain. Computed tomography scan revealed a hemorrhagic mass in the superior pole of the right kidney, with a thrombus extending from the ureter to the bladder. She underwent cryotherapy of the renal mass, together with retrograde ureteral stent placement, developed hypotension and respiratory distress, spiked high-grade fever, and had a new pansystolic murmur over the mitral and aortic areas. Urine and blood culture grew C. kefyr. Transthoracic echocardiogram revealed large mitral valve vegetation with moderate regurgitation. Micafungin was started, patient responded, and fungemia cleared. Repeat echocardiogram showed small vegetation, preserved leaflet mobility and mild regurgitation. Patient received 10 days of micafungin, followed by 6 weeks of fluconazole.
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PMID:Candida kefyr endocarditis in a patient with hypertrophic obstructive cardiomyopathy. 2008 70