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Query: UMLS:C0403608 (ureter)
 9,655 document(s) hit in 31,850,051 MEDLINE articles (0.00 seconds)

Multicystic renal dysplasia in a crossed fused or nonfused ectopic kidney is a rare occurrence that produces unusual imaging findings. In four such cases in neonates, three presented with a palpable abdominal mass and one was discovered in utero with maternal sonography. In three cases, sonography showed a multicystic mass, contiguous with the lower pole of the orthotopic kidney. In the fourth infant, a crossed, tiny dysplastic kidney was not visualized, but its markedly dilated ectopic ureter was seen traversing the spine on CT. Ureteropelvic junction obstruction was present in the three fused orthotopic kidneys. The characteristic imaging findings of multicystic dysplasia and crossed renal ectopia include a multicystic mass of variable size that is contiguous with the lower pole of a hydronephrotic, malrotated kidney; ureteral displacement and/or dilatation; and contralateral absence of the kidney and its renal artery.
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PMID:Multicystic dysplasia and crossed renal ectopia. 330 Feb 26

Multicystic kidney (MK) was diagnosed in 13 patients at the University Central Hospital of Oulu during the 9 year period 1970--78. In the district of the hospital the evaluated incidence of MK was 0.3 per 1000 live-born children. 12 of the patients were infants aged under one year. Two of these died soon after birth; one had severe extraurinary anomalies and the other had bilateral MK. The removal of MK was performed in ten cases. In ten operated and two autopsied patients the cystic dysplasia involved the kidney entirely. There was no discernible normal renal parenchyma and the ipsilateral ureter was always abnormal. On the opposite side one patient had a severe ureteric stenosis with hydronephrosis, and 4 patients had vesicoureteral reflux. Extraurinary anomalies were also common. Three patients had a significant cardiovascular abnormality. The accurate diagnosis could usually be obtained preoperatively. It was found that typical findings of physical examination, plain films, intravenous urography and B-mode ultrasound give sufficient information for accurate diagnosis to be made in most cases. Mictiocystography and endoscopy were required for associated urinary anomalies. Following the diagnosis, the removal of MK should be performed at the correct time, and also if asymptomatic, because these can become symptomatic later in life.
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PMID:Multicystic kidney. A clinical and histological study of 13 patients. 737 31

Multicystic dysplastic kidney (MCDK) is the most common renal cystic disease in infancy and the second most common neonatal abdominal mass. It represents an extreme form of renal dysplasia. The key features in MCDK include variability in size, loss of kidney shape, absence of function and obstruction of ureter. Current management is still controversial. The prognosis is largely depended upon the problems of associated anomalies and the condition of the contralateral kidney. From September '82 to September '91, twelve patients with multicystic kidney have been treated at Taichung Veterans General Hospital. Ten of them received elective nephrectomy. The postoperative condition was uneventful. However, there was a high frequency of associated anomalies (41.6%) and pathologic contralateral kidney (50%). Two patients who refused operation were put on close observation and follow-up with ultrasound. During the surgical patients' follow-up period, one suffered from repeated urinary tract infection and the other died of multiple congenital anomalies.
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PMID:The multicystic dysplastic kidney in children. 833 62