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Query: UMLS:C0027819 (neuroblastoma)
 27,800 document(s) hit in 31,850,051 MEDLINE articles (0.00 seconds)

The Authors stress the importance of a correct sonographic study in the follow-up of neonatal adrenal hemorrhage; the diagnostic conclusion are: the best criterion for differential diagnosis is the chronological variability. However the differential diagnosis is rather easy. The differential d. usually is against cystic-neuroblastoma, cortical renal cyst, adrenal abscess. They remark that laparatomy is unnecessary.
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PMID:[Hematoma of the adrenal gland in the newborn infant. Clinical course. Presentation of 20 cases]. 183 49

Fourteen cases are reported of monolateral adrenal hemorrhage in newborns who were submitted to US exam at 1 week, 2 weeks, 3 weeks, and 3 months of age. The variability is emphasized of US and pathologic findings according to the patients' age. A concise terminology is suggested allowing the description of morphological and echo-structural patterns in adrenal hemorrhage. Being familiar with US spectrum of neonatal adrenal hemorrhage appearances can provide useful data in the cases with atypical clinical features. Moreover, the differential diagnosis becomes easier of neonatal adrenal hemorrhage and other diseases such as neonatal neuroblastoma, adrenal abscess, cystic neuroblastoma, cortical renal cyst, and obstructed upper cortical renal cyst, and obstructed upper excretory tract in duplicated kidney. The most effective criterion for US differential diagnosis is probably the chronological variability of US findings. Sonography is stressed as an useful and effective imaging modality in the diagnosis and follow-up of adrenal hemorrhage which helps avoid X-ray investigations and unnecessary laparotomies.
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PMID:[Echography in the follow-up of neonatal adrenal hemorrhage. The presentation of 14 cases]. 219 24

We present eight cases of suprarenal masses detected sonographically in fetuses of 20-41 weeks. The appearances of the masses included hyperechoic (n = 2, both pulmonary sequestrations), solid isoechoic (n = 1, a neuroblastoma), purely cystic (n = 3, two neuroblastomas, one enteric cyst) and mixed or complex (n = 2, one neuroblastoma and one renal cyst). Three of the fetuses with neuroblastoma had normal scans in the second trimester, and in all four the neuroblastomas were detected after 36 weeks. This study demonstrates the differential diagnosis of suprarenal masses in fetuses. Neuroblastomas can have a solid, purely cystic or complex sonographic appearance. Although not all suprarenal masses are neuroblastomas, the newborn with a prenatally detected suprarenal mass should be evaluated for the possibility of a neuroblastoma, since early diagnosis of this malignancy can be curative.
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PMID:Fetal suprarenal masses: sonographic appearance and differential diagnosis. 778 90

Cystic kidney disease includes a wide range of hereditary, developmental, and acquired conditions of the kidneys. Some of the inherited causes of cystic kidney disease include autosomal dominant polycystic kidney diseases (caused by mutations in PKD1 or PKD2), autosomal recessive polycystic kidney disease, tuberous sclerosis complex, von Hippel-Lindau disease, oral-facial-digital syndrome type I, and Hadju-Cheney syndrome. Acquired cystic kidney disease has been reported in patients receiving long-term hemodialysis or peritoneal dialysis and in children after liver transplantation. Acute kidney injury can occur in patients with neuroblastoma, usually as a result of thrombotic microangiopathy associated with bone marrow transplantation. End-stage renal disease is described in long-term survivors. However, in this case report, we provide what is to our knowledge the first description of multiple kidney cysts in long-term survivors of stage IV neuroblastoma. None of the 7 patients we describe with neuroblastoma and multiple kidney cysts had a family history of autosomal dominant polycystic kidney disease. Also, all lacked stigmata of tuberous sclerosis complex, von Hippel-Lindau disease, or Hadju-Cheney syndrome. Two patients progressed to end-stage renal disease; in addition, one of them developed an oncocytoid renal cell carcinoma.
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PMID:Acquired Multiple Cysts of the Kidney in Neuroblastoma Survivors. 2701 49