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Target Concepts:
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Query: UMLS:C0024591 (
malignant hyperthermia
)
2,353
document(s) hit in 31,850,051 MEDLINE articles (0.00 seconds)
We present here the case of a 33-month-old male patient with
Wolf-Hirschhorn syndrome (WHS)
and who underwent tympanoplasty and myringotomy.
WHS
is caused by a rare chromosomal abnormality, which is the deletion of the short arm of chromosome number 4. The typical craniofacial features of
WHS
patients such as micrognathia, microcephaly and the muscular weakness can make using neuromuscular blocking agents and performing intubation difficult. Moreover, there are a few previous case reports showing that
malignant hyperthermia
occurred during and after an operation in which the anesthesia was done with inhalation agents, so special anesthetic care is needed when operating on a
WHS
patient. By carefully intubating the patient and using total intravenous anesthesia, we performed successful anesthesia without any complications. We describe here the anesthetic management of a
WHS
patient and we review the relevant literature.
...
PMID:Anesthetic experience using total intra-venous anesthesia for a patient with Wolf-Hirschhorn syndrome -A case report-. 2139 Jan 67
