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Query: UMLS:C0019270 (hernia)
 15,856 document(s) hit in 31,850,051 MEDLINE articles (0.00 seconds)

Beginning with a very vulgar symptomatology evoking with an adult, free from traumatic antecedents, a left ethmoido-maxillo-choanal polyp, the anatomo-pathologic survey of the lump, cutted out without incident, by the maxillary sinus (Caldwell-Luc), revealed the presence of zone of cerebral texture. The complaints of aqueous rhinorrhea increased and aggraved with diverse neuro-radiologic investigations enabled to state diagnostic of meningoencephalocele through ethmoidal left forepart osseous breach that was found and stopped up after by intracranial way. After this observation, the authors, looking at some generalities about meningoencephaloceles, insist on the frequency of the first manifestations generally from the first childhood, on the precious interest of the radiology in order to detect the osseous dehiscence and on the importance of neurosurgical exploration by intracranial mean before any endeavor of biopsy or of extraction of the lump by natural way. The originality of the reported case consist in the lack of symptomatology and in the late apparition of it, in the absence of septic meningitis complications after the extraction of the growth by low way (post-operative antibiotherapy), in the extention, unusual for the pharyngo-nasal kind of the cerebral hernia, into the maxillary sinus.
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PMID:[A case of a naso-sinus meningoencephalocele]. 121 89

Cephalocele is a rare lesion mainly of congenital or traumatic origin. The lesion occurs as an extracranial hernia of dura mater that consists of cerebrospinal fluid only (meningocele) or cerebellar tissue (encephalocele). Some cephaloceles concern anterior cranial fossa and then are observed as hernias in nasal cavity or in paranasal sinuses. Three patients are presented. In 52 year woman, who was admitted due to idiopathic rhinorrhea (persisting 16 years) with periodical headache, the meningocele in right ethmoid sinus was diagnosed. The lesion was removed with the rhinosurgical approach and the defect in anterior cranial fossa was repaired with the free cartilaginous flap. 12 year boy was admitted due to the nasal tumor diagnosed by CT and MRI. The lesion was removed with the combined access: firstly the hernia sac was cut intracranially with the frontal craniotomy and then encephalocele was removed with lateral rhinotomy. Cranial fossa defect was repaired by the periosteum flap. In third case (8 year boy) encephalocele caused 5 incidences of purulent meningitis. CT and MRI showed the lesion in frontal sinus. Encephalocele was removed with rhinosurgical approach and the defect in posterior frontal wall was repaired with free cartilaginous and mucosal flaps. In all patients long term result of operations was good. Anatomic and pathologic conditions that influence on the choice of rhinosurgical or combined access to nasal and sinusal encephaloceles are presented and discussed.
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PMID:[Meningoencephalocele as rhinosurgical problem]. 1452 81

A 14-year-old girl presented with chronic headache, recurrent episodes of vomiting, fever, and two episodes of generalized tonic clonic seizure in the past 2 months. Neuroimaging revealed herniation of the brain along with the dura through a defect in the left greater wing of the sphenoid. Left pterional craniotomy was carried out. Herniation of the dural sac along with its contents through the bony defect in the greater sphenoid wing was identified lateral to the V2 nerve passing through the foramen rotundum. The dural defect was repaired. Bony defect was covered with a circular titanium plate. The patient did not have cerebrospinal fluid rhinorrhea postoperatively. At 6-month follow-up, she was asymptomatic.
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PMID:A Rare Case of Sphenoid Encephalocoele Presenting with Fifth Cranial Nerve Involvement. 3243 2