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Query: UMLS:C0018799 (heart disease)
 34,133 document(s) hit in 31,850,051 MEDLINE articles (0.00 seconds)

This is a case report of an unusual clinical entity-the Straight Back Syndrome (SBS), in a two and a half (2 1/2) year old cerebral palsied Ghanalan male child. It was an incidental finding in which his lateral x-ray of the chest revealed a straight thoracic spine, devoid of the normal thoracic concavity. Organic heart disease was excluded by his normal electrocardiogram (EGG) and echocardiogram. Review of the literature shows that whereas in the sixties, this syndrome bore no associations with structural heart diseases, in the nineties, there have been significant organic heart defects described as its associates. The reports are however, silent on any association between cerebral palsy and the straight back syndrome.
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PMID:Straight-back syndrome. A case report and review of the literature. 762 38

Straight back syndrome is characterized by loss of the normal upper thoracic kyphosis, leading to a reduced anteroposterior diameter and squashing of the heart. Most patients are asymptomatic; if symptomatic, chest pain and palpitations are most common. On examination, the abnormal clinical findings simulate organic heart disease that needs to be ruled out by echocardiography and cardiac catheterization. A lateral chest radiograph is diagnostic. This condition is commonly associated with mitral valve prolapse and bicuspid aortic valve. We describe an interesting case of straight back syndrome with all the classic and rarely reported clinical findings.
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PMID:An interesting case of straight back syndrome and review of the literature. 2490 31