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Query: UMLS:C0012833 (dizziness)
 9,689 document(s) hit in 31,850,051 MEDLINE articles (0.00 seconds)

A rare case with coexistent extracranial congenital arteriovenous malformation and aneurysms of the occipital artery is presented. A 32-year-old man visited Tachikawa National Hospital with the complaints of occasional dizziness and a gradually growing pulsatile mass in the left occipital region. The patient had had no head trauma. Neurological examination revealed no abnormality. Physical examination showed a round and pulsating tumor measuring 4 cm x 7 cm in the retroauricular region on the left side, which lost its pulsation and consistency upon compressing the left common carotid artery. Left selective external carotid angiography demonstrated a tortuous and locally enlarged occipital artery with venous drainage around the artery and an arteriovenous malformation (AVM) in the retroauricular region and neck. The patient was successfully treated by surgical embolization of the feeding arteries with ligation of the left external carotid artery and partial excision of aneurysms under general endotracheal anesthesia. The postoperative course was uneventful. Fourteen months after the operation there is no evidence of recurrence of the pulsatile mass and the preoperative symptoms. Microscopic examination of the excised artery and aneurysms showed partial disappearance of the internal elastic lamina and muscle layer of the artery. Capillary nevi noted over the ear, retroauricular region, neck, and shoulder on the left side without history of head trauma and angiographic findings suggest that the AVM was congenital. In addition, we think that the aneurysms of the left occipital artery on the side ipsilateral to the AVM may have originated from the site of the arterial wall lacking the internal elastic lamina and developed due to hemodynamic mechanism associated with the AVM. Although the treatment of choice for extracranial, congenital and traumatic, AVMs is ideally total excision, careful embolization of the nidus with ligation of the feeders seems to be the most opportune procedure of choice as the second-best treatment in cases in which the nidus of the AVM occupies extensive areas of the head or face and which have little chance of developing serious signs and symptoms such as massive hemorrhage.
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PMID:[Coexistent congenital arteriovenous malformation an aneurysms of the scalp (author's transl)]. 729 Mar 22

Blue rubber bleb nevus syndrome is a rare disorder that is characterized by multiple recurrent vascular malformations, such as hemangioma, and these primarily involve the skin and the gastrointestinal tract. It may also involve the brain, liver, lungs, and skeletal muscles. A 14-year-old female visited our hospital with a chief complaint of dizziness; upon examination, we found multiple recurrent hemangiomas on the skin and gastrointestinal tract. We were able to diagnose her as suffering from blue rubber bleb nevus syndrome and we treated her with methylprednisolone (2 mg/kg/day for 1 month and 1 mg/kg/day for additional 3 months). We report on this case along with a review of the literature.
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PMID:A case of blue rubber bleb nevus syndrome. 1911 58

A 49-year-old woman presented with occipital headaches, dizziness, photophobia and vomiting for 2 weeks' status post posterior scalp mole removal by a general surgeon. The physical examination revealed occipital lesions with foul smelling purulent discharge mixed with clear fluid drainage, webbed neck with decreased range of motion, facial asymmetry and a low posterior hairline. A CT of head showed occipital skull defect providing a communicating pathway for scalp infection, an atlas fusion defect and an extensive pneumoencephaly. Further imaging showed low-lying cerebellar tonsils and fusion of the body of second and third cervical vertebrae. Klippel-Feil syndrome was diagnosed and the patient was successfully managed with duraplasty of occipital dura, placement of a lumbar drain and antibiotics. In patients with findings suggestive of Klippel-Feil syndrome and lesions proximal to the CNS, appropriate neuroimaging and possible neurosurgical consult should be considered prior to any surgical intervention.
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PMID:Postsurgical pneumoencephaly in a patient with Klippel-Feil syndrome. 2442 49