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Query: UMLS:C0002986 (Fabry)
 5,646 document(s) hit in 31,850,051 MEDLINE articles (0.00 seconds)

A short PQ interval is a common finding in patients with Fabry disease. However, there have been few electrophysiological studies in Fabry disease, and it is not clear whether the short PQ interval that is present in this disease results from preexcitation or enhanced atrioventricular nodal conduction. We present a case of a 43-year-old man with syncope, sick sinus syndrome, a PQ interval of 80 ms, and palpitations. Electrophysiological study showed PA, AH, and HV intervals of 24, 32, and 34 ms, respectively, and features of enhanced atrioventricular nodal conduction. The presence of an atrioventricular accessory pathway was excluded. We conclude that the short PQ interval in Fabry disease can result from accelerated conduction in the atrioventricular node.
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PMID:Electrophysiological study in a patient with Fabry disease and a short PQ interval. 1709 78

Theoretical and experimental analyses of piezoelectric stacks submitted to periodical electrical boundary conditions via electrodes are conducted. The presented structures exhibit Bragg band gaps that can be switched on or off by setting electrodes in short or open circuit. The band gap frequency width is determined by the electromechanical coupling coefficient. This property is used to design a Fabry-Perot cavity delimited by a periodic piezoelectric stack. An analytical model based on a transfer matrix formalism is used to model the wave propagation inside the structure. The cavity resonance tunability is obtained by varying the cavity length (i.e., by spatially shifting boundary conditions in the stack). 26% tuning of resonance and antiresonance frequencies with almost constant electromechanical coupling coefficient of 5% are theoretically predicted for an NCE41 resonator. To optimize the device, the influence of various parameters is theoretically investigated. The cavity length, phononic crystal (number and length of unit cells), and transducer position can be adapted to tune the frequency shift and the coupling coefficient. When the transducer is located at a nodal plane of the cavity, the value of the coupling coefficient is 30%. Experimental results are presented and discussed analyzing the effects of damping.
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PMID:Theoretical and experimental analyses of tunable Fabry-Perot resonators using piezoelectric phononic crystals. 2606 46

Recent experiments have shown that proximity with high-temperature superconductors induces unconventional superconducting correlations in graphene. Here, we demonstrate that those correlations propagate hundreds of nanometers, allowing for the unique observation of d-wave Andreev-pair interferences in YBa_{2}Cu_{3}O_{7}-graphene devices that behave as a Fabry-Perot cavity. The interferences show as a series of pronounced conductance oscillations analogous to those originally predicted by de Gennes-Saint-James for conventional metal-superconductor junctions. The present demonstration is pivotal to the study of exotic directional effects expected for nodal superconductivity in Dirac materials.
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PMID:Long-Range Propagation and Interference of d-Wave Superconducting Pairs in Graphene. 3290 64