Gene/Protein Disease Symptom Drug Enzyme Compound
Pivot Concepts:   Target Concepts:
Query: EC:1.3.1.8 (acyl-CoA dehydrogenase)
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Human Gene/Protein
FAM78A protein 15.3
acyl-CoA dehydrogenase 15.3
mitochondrial trans-2-enoyl-CoA reductase 15.3
ACAD9 protein 14.9
acyl-CoA dehydrogenase 9 14.8
SBCAD 14.7
ACAD11 14.6
SACM1L 14.3
CDK5 regulatory subunit-associated protein 1 14.3
Rrh 14.3
NADH dehydrogenase flavoprotein 1 14.3
hSCAD 14.2
ETFDH 13.9
ETFB 13.9
ACADSB 13.9
isobutyryl-CoA dehydrogenase 13.7
acyl-CoA synthetase family member 2 13.7
ACSM4 13.7
long chain acyl-CoA dehydrogenase 13.7
FLAD1 13.6
Isovaleryl-CoA dehydrogenase 13.6
ETFA 13.5
ACAD9 13.4
very-long-chain acyl-CoA dehydrogenase 13.4
OXSM 13.3
electron transfer flavoprotein ubiquinone oxidoreductase 13.3
ACAD10 13.2
electron transfer flavoprotein-ubiquinone oxidoreductase 13.1
M/SCHAD 13.1
isovaleryl-CoA dehydrogenase 13.1
short-chain acyl-CoA dehydrogenase 13.1
ETF-QO 13.1
ubiquinol-cytochrome c reductase binding protein 13.0
DECR 12.8
ACAD8 12.8
GPR172B 12.5
SCAD 12.4
long-chain acyl-CoA dehydrogenase 12.4
MCAD 12.3
CABC1 12.3
NDUFB5 12.3
medium-chain acyl-CoA dehydrogenase 12.3
apolipoprotein A-I binding protein 12.1
VLCAD 12.1
Medium-chain acyl-CoA dehydrogenase 12.0
glutaryl CoA dehydrogenase 12.0
ACOXL 12.0
elongation of very long chain fatty acids protein 12.0
2,4-dienoyl-CoA reductase 12.0
ETF 11.9
beta-ETF 11.9
iron-sulfur protein 3 11.8
very long-chain acyl-CoA synthetase 11.8
COQ6 11.8
enoyl-CoA hydratase 11.8
alpha-actinin 2 11.7
SCHAD 11.7
PDSS2 11.7
dienoyl-CoA isomerase 11.6
ACADM 11.6
DC12 11.5
mitochondrial 3-oxoacyl-CoA thiolase 11.4
ADCK3 11.4
N111 11.3
COQ9 11.3
3-ketoacyl-CoA thiolase 11.2
glutaryl-CoA dehydrogenase 11.2
3-hydroxyacyl-CoA dehydrogenase 11.1
ADCK4 11.1
UQCRB 11.1
COQ4 11.1
PDC2 11.1
dimethylglycine dehydrogenase 11.0
SLC16A12 11.0
ACSF3 11.0
DDRGK1 10.9
NDUFAF1 10.8
GA II 10.8
podocalyxin-like protein 10.8
MADD 10.8
more...
Disease
Disorders of mitochondrial metabolism 13.3
MCAD deficiency 12.8
Jordan's anomaly 12.1
Fatty acid oxidation defects 12.0
glutaric aciduria 11.0
HMG-CoA lyase deficiency 11.0
Fazio-Londe 10.8
Reye 10.2
Conduction disorders 9.5
riboflavin deficiency 9.4
Complex I deficiency 9.4
pediatric disorder 9.1
Reye's syndrome 8.7
Acute fatty liver of pregnancy 8.7
lipidosis 8.6
GA I 8.3
hyperglycinemia 8.2
propionic acidemia 8.1
McArdle's disease 8.1
PKS 7.8
Forbes 7.8
LWS 7.7
paramyotonia 7.7
thalassemia minor 7.5
IVA 7.4
maple syrup urine disease 7.4
protein deficiency 7.3
hypoglycemic coma 7.2
enzyme deficiency 7.2
EMA 7.2
ornithine transcarbamylase deficiency 7.1
Canavan 7.1
homocystinuria 7.0
myopathy 6.9
metabolic disorder 6.8
LQT1 6.8
attention deficit disorder 6.6
RP11 6.6
AMD 6.5
ASAT 6.5
gangliosidosis 6.5
leukodystrophy 6.4
neonatal asphyxia 6.3
ketosis 6.3
hypoglycemia 6.3
neuronal ceroid lipofuscinosis 6.3
CNF 6.2
SCD 6.1
MCD 6.1
mitochondrial disease 6.0
neuromuscular disorder 6.0
Angiostrongylus cantonensis 5.9
methylmalonic acidemia 5.9
Leigh syndrome 5.8
varicocele 5.8
tetany 5.7
lipid disorder 5.7
phenylketonuria 5.7
galactosemia 5.6
PND 5.6
MSA 5.6
orf 5.5
developmental delay 5.5
vitamin E deficiency 5.5
fatty liver 5.4
Leber's hereditary optic neuropathy 5.4
FFM 5.4
lactic acidosis 5.3
mitochondrial myopathy 5.2
Moore 5.2
major depressive episode 5.2
limb-girdle muscular dystrophy 5.2
failure to thrive 5.1
mucopolysaccharidosis 5.1
sinus tachycardia 5.0
Beckwith-Wiedemann syndrome 5.0
sudden infant death syndrome 4.9
oligohydramnios 4.8
petechiae 4.8
cardiomyopathy 4.8
more...
Symptom
Positive and Negative Symptoms 8.7
Spots 6.5
hypotonia 6.3
hepatomegaly 5.6
muscle cramps 5.5
hypertonia 5.0
myalgia 4.9
lethargy 4.8
weakness 4.7
stridor 4.1
starvation 4.0
vomiting 3.7
dysarthria 3.4
hyperoxia 3.0
exhaustion 2.6
seizures 2.5
ataxia 2.4
regurgitation 2.3
nausea and vomiting 2.1
sleepiness 1.7
fatigue 1.6
dyspnea 1.5
hypothermia 1.2
respiratory distress 1.0
angina 0.9
nausea 0.8
collapse 0.5
diarrhea -0.5
pain -2.7
Drug
Rifater 10.9
Rifater 10.8
Sodium phenylbutyrate 10.5
Riboflavin 9.4
FAD 8.9
Tween 60 7.6
Palmitoyl 7.1
SMP 6.7
Rosiglitazone 6.6
Glutamic acid 6.3
PFA 5.3
NADH 5.1
RFP 5.1
Serum albumin 5.0
Glycyrrhiza 4.8
Estrogens 4.2
citric acid 4.0
pyridoxal phosphate 4.0
ALA 3.8
Retinoic acid 3.6
Kenyan 3.5
Gel 3.4
ROS 3.4
ABC 3.2
lysine 2.9
Glutathione 2.9
CAM 2.8
MAP 2.4
THF 2.3
DNase I 2.3
Ethanol 2.1
CTX 2.0
Asn 1.8
Leaf 0.9
Enzyme
acyl-CoA dehydrogenase 15.3
acyl-CoA dehydrogenase 14.4
EC 1.3.1.44 14.3
electron transfer flavoprotein dehydrogenase 13.6
branched-chain acyl-CoA dehydrogenase 13.2
isovaleryl-CoA dehydrogenase 13.1
anthranilate hydroxylase 13.0
anthranilate hydroxylase 13.0
melilotate hydroxylase 12.7
trans-2-enoyl-CoA reductase 12.7
butyryl-CoA dehydrogenase 12.5
anthranilate hydroxylase 12.2
4-N-trimethylaminobutyraldehyde dehydrogenase 12.1
2,4-dienoyl-CoA reductase 12.1
isobutyryl-CoA mutase 12.0
desulfinase 11.8
geranoyl-CoA carboxylase 11.7
glutaconyl-CoA decarboxylase 11.3
acyl-CoA elongase 11.2
glutaryl-CoA dehydrogenase 11.1
3-hydroxyacyl-CoA dehydrogenase 11.1
EC 3.1.2.14 11.1
EC 5.3.3.8 11.1
dimethylglycine dehydrogenase 11.0
3-hydroxyacyl-CoA dehydrogenase 10.9
long-chain acyl-coenzyme A dehydrogenase 10.9
acyl-CoA oxidase 10.8
ECH 10.7
3-hydroxybutyryl-CoA dehydrogenase 10.6
3-hydroxyacyl-CoA epimerase 10.5
NAO 10.4
glycine N-acyltransferase 10.3
3-hydroxy-3-methylglutaryl-CoA lyase 10.0
KAT 10.0
acyl-CoA synthetase 9.9
ornithine cyclodeaminase 9.9
ribulose 5-phosphate 3-epimerase 9.8
p-hydroxybenzoate hydroxylase 9.6
acyl-CoA synthetase 9.6
p-hydroxybenzoate hydroxylase 9.5
sarcosine dehydrogenase 9.5
malonyl-CoA decarboxylase 9.1
LipB 9.1
butyrate kinase 8.9
aromatic amino acid aminotransferase 8.8
heterodisulfide reductase 8.7
SsuE 8.7
citrate synthase 8.6
propionyl-CoA carboxylase 8.5
AlkA 8.5
HMG-CoA synthase 8.4
membrane-bound hydrogenase 8.3
riboflavin kinase 8.3
methylmalonyl-CoA mutase 8.2
phosphoserine phosphatase 8.2
CPT 8.2
carnitine acetyltransferase 8.2
isocitrate lyase 8.2
fatty-acid synthase 8.0
acetoacetyl-CoA thiolase 8.0
ubiquinol-cytochrome c oxidoreductase 7.9
propionyl-CoA carboxylase 7.9
malate synthase 7.9
cystathionine gamma-synthase 7.8
lactate oxidase 7.8
beta-hydroxybutyrate dehydrogenase 7.7
aspartoacylase 7.7
phosphoglyceromutase 7.7
biotinidase 7.7
acyl carrier protein synthase 7.6
succinyl-CoA synthetase 7.6
EC 1.1.1.40 7.6
acetyl-CoA carboxylase 7.5
branched-chain aminotransferase 7.5
mercuric reductase 7.4
pantothenate kinase 7.4
fatty acid elongase 7.3
dihydropyrimidinase 7.2
conjugase 7.2
fumarylacetoacetate hydrolase 7.1
more...
Compound
2-methylmalonamide 15.3
4-cis-Decenoyl-CoA 15.3
Crotonyl-CoA 14.1
octanoyl-CoA 13.4
undecylbenzene 13.3
Ethylmalonic acid 13.0
Decanoyl-CoA 12.7
butyryl-CoA 12.2
3-Hydroxyglutaric acid 12.1
Hypoglycin A 12.0
MEZ 11.7
tetradecanedioic acid 11.6
5-hydroxyhexanoic acid 11.3
10-hydroxydecanoic acid 11.1
3-methylcrotonyl-CoA 11.0
10-hydroxydecanoic acid 11.0
3-hydroxybutyryl-CoA 10.9
Kirromycin 10.8
Biguanide 10.5
propionyl-coenzyme A 10.5
glutaryl-CoA 10.4
acetoacetyl-CoA 10.1
palmitoyl-CoA 9.9
Normetanephrine 9.8
hexanedioic acid 9.8
3-buten-2-one 9.5
3-hydroxyoctanoic acid 9.4
hexanedioic acid 9.4
Riboflavin 9.4
CoA 9.4
3-buten-2-one 9.3
4-heptanone 9.3
Acyl-CoA 9.1
4-pentenoic acid 9.0
FK520 9.0
6-APA 8.9
3-heptanone 8.9
FAD 8.9
3-heptanone 8.8
9,12-octadecadienoic acid 8.8
2-ethylhexanoic acid 8.8
2-ethylhexanoic acid 8.8
dodecanedioic acid 8.8
2-ethylhexanoic acid 8.8
Mercaptopropionic acid 8.7
3-heptanone 8.7
suberic acid 8.6
decanoic acid 8.5
2-ethylhexanoic acid 8.4
pimelic acid 8.4
Piperidine 8.3
decanoic acid 8.3
WY-14,643 8.2
FMN 8.1
Carnitine 8.0
3-hydroxyisovaleric acid 7.9
Sesamin 7.8
malonyl-CoA 7.7
L-carnitine 7.7
acetyl-CoA 7.7
dihydrolipoamide 7.7
MAD 7.6
GBL 7.6
Salinomycin 7.5
hexanoic acid 7.4
pentadecane 7.4
methanethiol 7.4
heptanoic acid 7.4
isonicotinamide 7.4
CoQ 7.3
azelaic acid 7.3
hexanoic acid 7.3
heptanoic acid 7.3
octanoic acid 7.3
octanoic acid 7.3
octanoic acid 7.3
Pinacidil 7.2
octanoic acid 7.2
Squalene 7.2
octanoic acid 7.1
more...